https://imcjms.com Ibrahim Medical College Journal of Medical Science https://imcjms.com/registration/journal_full_text/245 Sat, 08 Jul 2017 13:47:49 +0000 A 22 years male patient presented with gradual left forearm swelling for 6 months. X ray forearm revealed large soft tissue swelling with tiny calcification and mild scalloping at inner aspect of ulna and ultrasonogram (USG) revealed soft tissue mass having calcification and necrotic areas within and spectral Doppler showed arterial type of blood flow with no augmentation. Later computerized tomography (CT) scan showed soft tissue mass with necrotic area and calcification with no bony involvement. Magnetic resonance imaging (MRI) with contrast revealed a large heterogeneously enhancing lobulated mixed intensity lesion in antero-medial compartment of the left forearm involving flexor group of muscles causing displacement of fat plane. MRI and subsequent histopathology of the lesion revealed it as a rare soft tissue Ewing’s sarcoma / primitive neuroectodermal tumor (PNET) in extremity. 1.   Smoll, N.R. Relative survival of childhood and adult medulloblastomas and primitive neuroectodermal tumours (PNETs). Cancer 2012; 118(5): 1313-1322. 3.   Schajowicz F. Ewings sarcoma and reticulumn cell sarcoma of bone with special reference to the histochemical demonstration of glycogen as an aid to differential diagnosis. J Bone Joint Surg Am 1959; 41(2): 349-362. 5.   Siebenrock KA, Nascimento AG and Rock MG. Comparison of soft tissue Ewing’s Sarcoma and peripheral neuroectodermal tumour.Clinical Orthopaedics and Related Research 1996; 329:       288-299. 7.   Stout AP. A tumor of the ulnar nerve. Proc NY Pathol Soc 1918; 18: 2-11. 9.   Toro JR, Travis LB, Wu hj, Zhu K, Fletcher CDM and Devesa SS. Incid-ence patterns of soft tissue sarcomas, regardless of primary site, in the surveillance, Epidemiology and End Results Program.1978-2001: an analysis of 26,758 cases. International Journal of Cancer 2006; 119(12):      2922-2930. 11.Rud NP, Reiman HM, Pritchard DJ, Frassica FJ and Smithson WA. Ext-raosseous Ewing’s Sarcoma: A study of 42 cases. Cancer 1989; 64(7): 1548-1553. 12  Cotterill SJ, Ahrens S, Paulussen M, Jurgens HF, Voute PA, Gadner H and Craft AW. Prognostic factors in Ewing’s tumour of bone: Analysis of 975 patients from the European Intergroup Cooperative Ewing’s Sarcoma Study Group. Journal of clinical oncology 2000; 18(17): 3108-3114. 2026 Ibrahim Medical College. All rights reserved.